Galactosidase alpha Antibody / Gla | F54879-0.4ML

Galactosidase alpha Antibody / Gla | F54879-0.4ML | Gentaur US, UK & Europe Disrtribition

Family: Primary antibody

Formulation: In 1X PBS, pH 7.4, with 0.09% sodium azide

Format: Purified

Clone: N/A

Host Animal: Rabbit

Clonality: Polyclonal (rabbit origin)

Species Reactivity: Human

Application: FACS, IF, IHC-P, WB

Buffer: N/A

Limitation: This Galactosidase alpha antibody is available for research use only.

Purity: Purified

Description: GLA is a homodimeric glycoprotein that hydrolyses the terminal alpha-galactosyl moieties from glycolipids and glycoproteins. This enzyme predominantly hydrolyzes ceramide trihexoside, and it can catalyze the hydrolysis of melibiose into galactose and glucose. A variety of mutations in this gene affect the synthesis, processing, and stability of this enzyme, which causes Fabry disease, a rare lysosomal storage disorder that results from a failure to catabolize alpha-D-galactosyl glycolipid moieties.

Immunogen: A portion of amino acids 83-112 from the human protein was used as the immunogen for the Galactosidase alpha antibody.

Storage: Aliquot the Galactosidase alpha antibody and store frozen at -20 °C or colder. Avoid repeated freeze-thaw cycles.